Ependymal tumors are uncommon in intracranial tumors. Ependymal origin usually involves an intraventricular localization. Exceptional intraparenchymal extra ventricular locations have been described. We report a case of extra ventricular ependymoma managed in our department.
Case Description. An 8-year-old girl was admitted in January 2019 for left hemiparesis that had been progressing for two weeks associated with chronic headaches. Neurological examination noted a muscle strength rated at 4/5 in left hemi body. Medical imaging made it possible to highlight a voluminous mixed, intraparenchymal, right parietal temporal mass first evoking diffuse astrocytoma (WHO grade II). After gross total excision, histology and immunohistochemistry concluded that it was WHO grade II ependymoma. At five months postoperatively, the patient was asymptomatic and control CT scan was unremarkable. After a 4-year follow-up, the patient remained asymptomatic.
Conclusion. Extra ventricular ependymoma diagnosis was a histological surprise. Surgical removal of this lesion was not a problem. Course was satisfactory in the absence of adjuvant therapy (chemo and/or radiotherapy).

ependymoma, extra ventricular, surgery